Hamman-Rich syndrome
Related people
Previously used term for acute diffuse idiopathic interstitial pulmonary fibrosis of unknown aetiology. Insidious onset followed by respiratory embarrassment, fatigability, loss of weight, cyanosis, right-sided heart failure and other abnormalities. It is usually fatal. Both sexes affected; slight male predominance; onset over broad age range, but highest incidence between 40 and 70 years of age. Aetiology unknown. Familial, autosomal dominant inheritance.
First described by Sir Dominic John Corrigan (1802-1880) in 1838, in 1897 by Georg Eduard Rindfleisch (1836-1908) as «cirrhosis cystica» and in 1915 by David Paul von Hansemann (1858-1920) as «lymphangitis reticularis».
Bibliography
- D. J. Corrigan:
On cirrhosis of the lung.
The Dublin Journal of Medical Science, 1838, 13: 266-286. - G. E. Rindfleisch:
Ueber Cirrhosis Cystica Pulmonum. Zentralblatt für allgemeine Pathologie und pathologische Anatomie, Jena, 1897, 8: 864–865. - L. Hamman, A. R. Rich:
A clinical-pathological conference. A case of heart failure.
International Clinics, 43d series, 1933: 1: 197-232 - L. Hamman, A. R. Rich:
Fulminant diffuse interstitial fibrosis of the lungs. Transactions of the American Clinical and Climatological Association, 1935, 51: 154-163. - L. Hamman, A. R. Rich:
Acute diffuse interstitial fibrosis of the lungs.
Bulletin of the Johns Hopkins Hospital, Baltimore, 1944, 74: 177-212. - S. Javaheri, D. H. Lederer, J.A. Pella, G. J. Mark and B.W. Levine:
Idiopathic pulmonary fibrosis in monozygotic twins: the importance of genetic predisposition. Chest, 1980, 78: 591-594.