Devergie's disease
Related people
- Claudius Tarral
- Ernest Henri Besnier
- Ferdinand Ritter von Hebra
- Marie-Guillaume-Alphonse Devergie
- Moriz Kohn Kaposi
A chronic mildly inflammatory, exfoliative disease of the skin affecting both sexes, with onset at any age. Characterized by dry, acuminate papules about 1 mm in diameter surrounding hair follicles with horny plugs and scales that dip into the follicle. Some cases begin in infancy, most commonly after 15 years of age.
Infantile form may be transmitted as an autosomal dominant trait. No demonstration of genetic factors in adult form.
The term Devergie’s disease was introduced by Ernest Henri Besnier (1831-1909) in 1889.
Bibliography
- M. G. A. Devergie:
Pityriasis pilaris, maladie de la peau non décrite par les dermatologistes.
Gazette hebdomadaire de médecine et de chirurgie, Paris, 1856, 3: 197-201. - E. Besnier:
Observations pour servis a l'histoire clinique de pityriasis rubra pilaris.
Annales de dermatologie et de syphilographie, Paris, 1889, 11: 253-287, 398-427, 485-544. - M. Kaposi:
Lichen ruber acuminatus und Lichen ruber planus.
Archiv für Dermatologie und Syphilis, Prague, 1895, 31: 1-32.